췌장외 점액누출을 동반한 췌관내 유두상 점액종양에 의한 복막 가성점액종 1예 |
김해수1, 원영웅1, 최정혜1, 유교상1, 여유미1, 이지영1, 표주연2, 박훤겸3 |
1한양대학교 구리병원 내과, 2한양대학교 구리병원 병리과, 3한양대학교 구리병원 외과" |
Pseudomyxoma Peritonei Caused by Intraductal Papillary Mucinous Neoplasm With Extra-pancreatic Mucin Leakage: A Case Report |
Hae Su Kim1, Young Woong Won1, Jung Hye Choi1, Kyo Sang Yoo1, Yoo mi Yeo1, Ji young Yhi1, Ju Yeon Pyo2, Hwon Kyum Park3 |
1Department of Internal Medicine, 2Department of Pathology and 3Department of Surgery, Hanyang University Guri Hospital, Guri, Korea |
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ABSTRACT |
Pseudomyxoma peritonei (PMP) is a rare clinical entity characterized by gelatinous tumor implants within the peritoneal cavity and a large amount of mucinous ascites. Although most PMP cases originate in the appendix, few are associated with pancreatic intraductal papillary mucinous neoplasm (IPMN). IPMNs secrete thick mucin; therefore, they usually present with pancreatic duct dilatation. The presence of IPMN with extra-pancreatic mucin could be a marker of the eventual seeding of tumor outside the primary site. PMP associated with mucin leakage from pancreatic IPMN has been rarely reported. Here, we report the case of a patient with PMP that originated from pancreatic IPMN. |
Keywords:
pseudomyxoma peritonei, intraductal papillary mucinous neoplasm (IPMN), pancreas, mucin |
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