Institute for Digestive Research, Department of Internal Medicine, Soonchunhyang University College of Medicine, Seoul, Korea
ABSTRACT
Immunoglobulin G4-associated sclerosing cholangitis (IAC) is a recently defined disease. IAC is a rare type of autoimmune pancreatitis associated with bile duct involvement, which can present with or without pancreatic involvement. Usually, multiple intra and extrahepatic manifestations is similar to that of primary sclerosing cholangitis. Rarely, there can be an isolated stricture which mimics cholangiocarcinoma. Though extremely difficult, differentiating these from cholangiocarcinoma is of critical importance because it can be treated without surgical intervention. We reported one such rare presentation of autoimmune pancreatitis in a 36 years old patient in whom photodynamic therapy (PDT) was done for a hilar stricture, which later turned out to be related to IAC.