Department of Internal Medicine, Hallym University Collage of Medicine, Seoul, Korea
ABSTRACT
Choledochal cysts are cystic dilations that may occur throughout the biliary tree. Choledochal cysts are associated with significant complications, such as ductal strictures, stone formation, cholangitis, rupture, and malignancy. Polycystic kidney disease is often associated with polycystic liver disease, but it has been rarely reported to be associated with choledochal cyst. A 32-year-old male entered hospital because of abdominal discomfort and epigastric pain. Computed tomography and magnetic resonance cholangiopancreatography showed multiple low density cystic lesions in entire liver and in both kidneys, and fusiform dilatation of common bile duct. We diagnosed this patient as autosomal dominant polycystic kidney disease and type I choledochal cyst. Our patient underwent a surgical operation. It was diagnosed as cholangiocarcinoma on tissue biopsy.