Department of Internal Medicine, Hallym University College of Medicine, Kangdong Sacred Heart Hospital, Seoul, Korea, 2Department of Pathology, Hallym University College of Medicine, Kangdong Sacred Heart Hospital, Seoul, Korea,
ABSTRACT
Idiopathic adulthood ductopenia (IAD) is a rare adult onset chronic cholestatic disease of unknown etiology without the existence of inflammatory bowel disease. IAD has characteristics of autoantibody absence in lab findings and loss of interlobular bile ducts in biopsy. A 28-year-old man admitted to the hospital with an incidental finding of elevated transaminases and alkaline phosphatase on routine health screening. The viral hepatitis markers and autoimmune hepatitis antibodies were all negative. The patient showed a radiologically normal anatomy of extrahepatic biliary tree. Histological examination of four liver biopsy specimens showed severe ductopenia on all portal tracts. We, herein, report a rare case of IAD with a brief review of literature.
PDF Links
Full text via DOI
Download Citation 
