내시경적 절제술로 치료된 바터팽대부 신경절세포 부신경절종 |
양해민1, 박현우1, 김선주2, 조창민1, 정민규1 |
경북대학교 의학전문대학원 내과학 교실
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A Gangliocytic Paraganglioma of the Ampulla of Vater Treated by Endoscopic Snare Papillectomy |
Hae Min Yang1, Hyun Woo Park1, Sunzoo Kim2, Chang Min Cho1, Min Kyu Jung1 |
1Department of Internal Medicine, Kyungpook National University School of Medicine, 2Department of pathology, Kyungpook National University Hospital |
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ABSTRACT |
Gangliocytic paraganglioma is an extremely rare tumor that is usually seen in the duodenum. It has unique histologic features composed of endocrine cells with a carcinoid-like appearance, isolated ganglion cells, and spindle-shaped Schwann cells. Generally, this tumor is considered benign, because only a few cases of regional lymph node metastases and local recurrence have been reported. But in most patients, resection, including pancreatoduodenectomy, was performed because preoperative diagnosis was difficult. We present a case of a gangliocytic paraganglioma of the ampulla of vater misdiagnosed as ampullary adenoma and treated with endoscopic papillectomy. The resected specimen revealed a gangliocytic paraganglioma. All margins of resection were negative for tumor. A size of the specimen was 2.0×1.3×1.0 cm. We present this case, because gangliocytic paraganglioma is a rare tumor, and it was successfully treated with endoscopic resection. |
Keywords:
Gangliocytic paraganglioma, Ampulla of Vater |
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